Klippel-Trenaunay-Weber Syndrome During Pregnancy

Abstract

Introduction: Klippel-Trenaunay-Weber syndrome is a congenital vascular malformation characterized by a classic clinical triad consisting of vascular anomalies, port-wine skin spots, and hypertrophy of soft and bone tissues.
Objective: To describe the case of a patient with Klippel-Trenaunay-Weber syndrome during pregnancy.
Case presentation: The case of a 41-year-old female, multiparous, multipregnant patient with history of chronic venous insufficiency and Klippel-Trenaunay-Weber syndrome is reported. During her pregnancy she presented two events of superficial varicothrombosis, one cellulitis, and her intraoperative and immediate postpartum period were marked by severe compensated preeclampsia. It was possible to perform a cesarean section at 39.3 weeks of gestational age and a live male newborn was obtained weighing 2600 g, Apgar test 8/9, small and calcified placenta, clear amniotic fluid and normal cord.
Conclusions: The coexistence of Klippel-Trenaunay-Weber syndrome during pregnancy makes it classified as a potential risk due to the morbidity it implies. This becomes a challenge for the obstetrician and his multidisciplinary team, which demands timely and correct management.