From the embryological basis to the clinical Prune Belly syndrome
Keywords:
Prune Belly syndrome, urethral obstruction, imperforate anus, cryptorchidism, abdominal agenesisAbstract
Prune Belly syndrome is a congenital disorder that is due, as currently reported, to genetic basis. It is characterized by the following triad: deficiency of abdominal muscles in varying degrees, bilateral cryptorchidism and urinary tract anomalies. Two variants of the syndrome are identified, a deadly one and another compatible with life.